Rinsho Shinkeigaku (Clinical Neurology)

Brief Clinical Note

A case of Marfan's syndrome with anterior sacral meningocele along with recurring bacterial meningitis

Akiko Hatano, M.D.1)2), Katsunori Akiyama, M.D.1)2), Masao Nagayama, M.D.3) and Shigeharu Takagi, M.D.1)

1)Department of Neurology, Tokai University School of Medicine
2)Department of Neurology, Tokai University Oiso Hospital
3)Department of Neurology, Yokohama Stroke and Brain Center

We reported a 46-year-old woman with Marfan's syndrome exhibiting an incomplete Currarino triad and recurrent bacterial meningitis which recurred three times in about six months. An anterior sacral meningocele (ASM) was noted in a lumbar MRI, and multiple bone defects in the sacrum were noted in 3D-CT. Surgical approach to prevent the recurrence of infection was limited to plasty for the meningocele, but no meningitis has been observed for two years. Radical surgery should be considered in cases with ASM who recurred bacterial meningitis.

(CLINICA NEUROL, 46: 658|660, 2006)
key words: Currarino triad, meningocele, recurrent bacterial meningitis, Marfan's syndrome

(Received: 10-Apr-06)